Case Reports
Management of soft palate agenesis in Nager syndrome with an elongated, superiorly based pharyngeal flap
Affiliations
- PMID: 25397380
Item in Clipboard
Case Reports
Management of soft palate agenesis in Nager syndrome with an elongated, superiorly based pharyngeal flap
Ear Nose Throat J.
2014 Oct-Nov.
Abstract
Nager syndrome, or preaxial acrofacial dysostosis, is associated with aberrant development of the first and second branchial arch structures, as well as abnormal development of the limb buds. It is a rare disorder, and its clinical manifestations have not been completely defined. Absence of the soft palate has been reported in patients with Nager syndrome. In this report we describe the use of an elongated, superiorly based pharyngeal flap for the treatment of severe velopharyngeal insufficiency in a patient with Nager syndrome and absence of the soft palate. We also describe the dysmorphisms associated with Nager syndrome and present a differential diagnosis for the condition.
Similar articles
-
Comparison of obstructive sleep apnea syndrome in children with cleft palate following Furlow palatoplasty or pharyngeal flap for velopharyngeal insufficiency.Cleft Palate Craniofac J. 2004 Mar;41(2):152-6. doi: 10.1597/02-162. Cleft Palate Craniofac J. 2004. PMID: 14989690
-
A technique for lining the palatopharyngeal flap with a single hinge flap.Ann Plast Surg. 1986 Dec;17(6):489-92. Ann Plast Surg. 1986. PMID: 3827118
-
The pharyngeal flap operation.Clin Plast Surg. 1985 Oct;12(4):697-710. Clin Plast Surg. 1985. PMID: 3905176
-
Surgical management of velopharyngeal insufficiency.Clin Plast Surg. 2014 Apr;41(2):253-70. doi: 10.1016/j.cps.2013.12.010. Clin Plast Surg. 2014. PMID: 24607193 Review.
-
Surgery for velopharyngeal insufficiency.Adv Otorhinolaryngol. 2012;73:137-44. doi: 10.1159/000334471. Epub 2012 Mar 29. Adv Otorhinolaryngol. 2012. PMID: 22472246 Review.
Publication types
MeSH terms
Supplementary concepts
LinkOut - more resources
Medical